Ebstein anomaly: Celermajer index
RA + aRV
f RV
LA
LV
Celermajer index, also known as the Great Ormond Street Echocardiography (GOSE) score: The end-diastolic areas measured in echocardiography or end-diastolic volumes assessed through cardiac magnetic resonance (CMR) were used according to the following formula:
Celermajer index = (right atrium + atrialized right ventricle) / (functional right ventricle + left atrium + left ventricle).
Based on this calculation, patients were classified into the following grades:
- Grade 1: Celermajor index < 0.5
- Grade 2: 0.5 to 0.99
- Grade 3: 1.0 to 1.49
- Grade 4: > 1.5
Result:
References
Cieplucha A, Trojnarska O, Bartczak-Rutkowska A, Kociemba A, Rajewska-Tabor J, Kramer L, et al. Severity Scores for Ebstein Anomaly: Credibility and Usefulness of Echocardiographic vs Magnetic Resonance Assessments of the Celermajer Index. Canadian Journal of Cardiology [Internet]. 2019 Dec 1;35(12):1834–41. Available from: https://www.sciencedirect.com/science/article/pii/S0828282X19311493